골격근 침범과 다발성 림프종성 용종증의 임상양상으로 나타난 Mantle Cell Lymphoma 1예 |
임현정·최바울·허진욱·김동완·이지영·박무인·박선자·이재화*·구자영 |
고신대학교 의과대학 내과학교실, *병리학교실 |
A Case of Mantle Cell Lymphoma Presenting as Multiple Lymphomatous Polyposis Involving Skeletal Muscles |
Hyun Jeung Lim, M.D., Paul Choi, M.D., Jin Wuk Hur, M.D., Dong Wan Kim, M.D., |
Departments of Internal Medicine and *Pathology, Kosin University College of Medicine, Busan, Korea |
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Abstract |
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Multiple lymphomatous polyposis (MLP) is an uncommon type of primary non-Hodgkin's gastrointestinal B cell-lymphoma characterized by the presence of multiple lymphomatous polyps along the gastrointestinal tract. Unlike MALT-lymphoma, MLP has a strong tendency for histologically monomorphic character, extra-digestive localization, rare lymphoepithelial lesion and poor prognosis. The malignant cells of MLP share morphological, immunohistologic and cytogenetic similarities with cells of node-based mantle cell lymphoma. We report a case of mantle cell lymphoma presenting with MLP involving various segments of the gastrointestinal tract, skeletal muscles of the right thigh and bone marrow observed in a 71-year-old woman who complained of lower abdominal pain and a palpable right thigh mass. (Korean J Gastrointest Endosc 2003;27:1520) |
Key Words:
Multiple lymphomatous polyposis, Mantle cell lymphoma |
주요어:
다발성 림프종성 용종증, 외투세포 림프종 |
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