| von Hippel-Lindau병 환자의 이중 비르숭관 췌장 1예 |
| 김혜수ㆍ한병훈ㆍ김선정ㆍ이지숙ㆍ박세진ㆍ이상욱ㆍ허방*ㆍ김정현† |
| 고신대학교 의과대학 내과학교실, *병리학교실, †성균관대학교 의과대학 삼성서울병원 진단검사의학교실 |
| A Case of Pancreatic Dual Wirsung Ducts in a Patient with von Hippel-Lindau Disease |
| Hye Soo Kim, M.D., Byung Hoon Han, M.D., Sun Jung Kim, M.D., Jee Sook Lee, M.D., Sae Jin Park, M.D., Sang Uk Lee, M.D., Bang Hur, M.D.* and Jung Hyun Kim, M.D.† |
| Departments of Internal Medicine and *Pathology, Kosin University College of Medicine, Busan, †Department of Laboratory Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea |
|
|
|
|
| Abstract |
|
|
Rare autosomal dominant disorders associated with various tumors and cysts, and several kinds of pancreatic lesions have been described in patients with von Hippel- Lindau (VHL) disease, but there have been few studies concerned with the variations of the pancreatic duct. We experienced a case of pancreatic dual Wirsung ducts in a patient with VHL disease. Computed tomography scans showed that multiple cysts had nearly completely replaced the pancreas, there was a solid tumor on the uncinate process of the pancreas and a left renal mass suggested renal cell carcinoma. ERCP shows that the Santorini duct and Wirsung duct were fused in a normal fashion, and another Wirsung duct had shrub-like branches that are commonly seen in pancreatic divisum. (Korean J Gastrointest Endosc 2008;37:384-388) |
| Key Words:
von Hippel-Lindau disease, Pancreas, Pancreatic duct, Dual Wirsung ducts |
| 주요어:
von Hippel-Lindau병, 췌장, 췌장관, 이중 비르숭관 |
|
|
PDF Links
Full text via DOI 
Download Citation 
