Korean Journal of Gastrointestinal Endoscopy 1991;11(2): 317-321.
선천성 감섬유증 1예 ( A Case of Congenital Hepatic Fibrosis )
최원, 전재윤, 이세준, 이돈행, 송시영, 이상인, 강진경, 박인서, 최흥재, 심원흠, 박찬일 (Won Choi, Chae Yoon Chon, Se Joon Lee, Don Haeng Lee, Si Young Song, Won Heum Shim, Sang In Lee, Jin Kyung Kang, In Suh Park, Heung Jai Choi and Chan Il Park)
Abstract
We experienced a case of congental hepatic fibrosis in a 21-year-old Korean male. He had frequent episodes of esophageal variceal bleeding. His liver and kidney functions were preserved. He had cystic lesions on both kidneys. A diagnosis of congenital hepatic fibrosis was made by an inferior venacavogram and peritoneoscopic liver biopsy. A Kobayashi operation was performed for esophageal varices. He had no more variceal bleeding and his general condition was good after operation.