Korean Journal of Gastrointestinal Endoscopy 1998;18(4): 561-566.
증례 : 식도 위장관 ; 위내시경으로 진단된 원발성 위 유전분증 1예 ( Case Reports : Esophagus , Stomach & Intestine ; A Case of Primary Gastric Amyloidosis Diagnosed by Endoscopy )
이석호, 이풍렬, 김재준, 이규택, 이준혁, 이종균, 손희정, 강인구, 오성윤, 고광철, 백승운, 이종철, 최규완, 오영륜 (Suk Ho Lee, Poong Lyul Rhee, Jae Jun Kim, Kyu Taek Lee, Joon Hyoek Lee, Jong Kyun Lee, Hee Jung Son, In Koo Kang, Sung Yun Oh, Kwang Cheol Koh, Seung Woon Paik, Jong Chul Rhee, Kyu Wan Choi and Young Lyun Oh)
Abstract
Amyloidosis is characterized by deposition of amyloid, which is resistant to proteolysis & phagocytosis, in intercellular spaces & vascular walls. The amyloid deposition provokes dysfunction of an accumulated organ & displays variable clinical symptoms depending upon the involved organ. A diagnosis is rendered through a biopsy of the affected organ, followed by staining using congo red which reveals an apple greenish refractile birefringence via polarizing microscopy. Using an electro-microscopy specific filaments can be found. Amyloidosis is classified into primary amyloidosis, composed of light chain filaments (AL) and secondary amyloidosis, comprised of A protain (AA). The AL type of amyloidosis shows deposition of amyloid in muscularis mucosa & muscularis externa. Priunary amyloidosis on the other hand, is relatively rare. We experienced primary stornach amyloidosis (AL), which was mistaken for stomch cancer. (Korean J Gastrointest Endosc 18: 561-566, 1998)
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