| A Case of Peutz-Jeghers Syndrome with Multiple Intussusception and Rectal Adenocarcinoma |
| Young-Hae Sohn, M.D., Young-Eun Joo, M.D., Kyoung-Won Yoon, M.D.,Sung-Bum Cho, M.D., Hyeong-Rok Kim, M.D.*, Young-Jin Kim, M.D.*,Hyun Soo Kim, M.D. and Sei Jong Kim, M.D. |
| Departments of Internal Medicine and *General Surgery, |
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| Abstract |
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Peutz-Jeghers syndrome (PJS) is a rare disease of autosomal dominant inheritance, which is characterized by hamartomatous gastrointestinal polyps and mucocutaneous melanin pigmentation. PJS often presents as surgical emergen cies with complications of the polyps, such as intussusception, small bowel obstruction, bleeding and volvulus. Intussusception caused by PJS polyps is often observed in the small bowel, but intussusception which involving small and large bowel concommittantly is not so much. The association between PJS and an increased risk for cancer has been controversial. Recent studies have shown PJS have a increased risk for both gastrointestinal and extraintestinal cancer. We report a case of PJS with rectal adenocarcinoma and multiple intussusceptions involving small and large bowel concommittantly. (Korean J Gastrointest Endosc 2001;22:220224) |
| Key Words:
Peutz-Jeghers syndrome, Intussusception, Rectal adenocarcinoma |
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